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Chapter 17 - Rheumatologic Disorders
Book chapter

Chapter 17 - Rheumatologic Disorders

Pediatric Hand Therapy, pp 229-242
2020

Abstract

Enthesitis-related arthritis (formerly juvenile spondyloarthropathy) Juvenile idiopathic arthritis Oligoarticular Oligoarticular onset with polyarticular course Polyarticular-rheumatoid factor negative Polyarticular-rheumatoid factor positive Psoriatic arthritis Systemic
Juvenile idiopathic arthritis is the most common inflammatory joint disorder in childhood and may cause substantial intraarticular damage, long-term joint sequelae, and eventual disability. Arthritis occurring with other inflammatory rheumatic disorders in childhood, such as systemic lupus erythematosus, juvenile dermatomyositis, mixed connective tissue disease, and progressive systemic sclerosis is most often milder and nonprogressive. If joint contractures and deformities develop with these latter disorders, they are most often the result of severe extraarticular, intracutaneous, or subcutaneous fibrosis rather than severe intraarticular disease.

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