Logo image
The Genetics Contributing to Disorders Involving Congenital Scoliosis
Book chapter   Open access

The Genetics Contributing to Disorders Involving Congenital Scoliosis

Nan Wu, Philip Giampietro and Kazuki Takeda
The Genetics and Development of Scoliosis, pp 89-106
13 Jun 2018
url
https://doi.org/10.1007/978-3-642-39345-7_15View
Published, Version of Record (VoR)Maybe Open Access (Publisher Bronze) Open

Abstract

Alagille Syndrome (ALGS) Ripply Spondylocostal Dysostosis VACTERL Association Vertebral Malformations
Congenital scoliosis (CS) is a congenital deformity of the spine, which can present as an isolated malformation, or part of a syndrome with other clinical features such as renal, cardiac, gastrointestinal, and limb malformations, etc. FGF, WNT, Notch, and TGFβ signaling pathway-associated genes have important roles in spine development. In this chapter, we highlight the embryologic basis of CS, including relevant genes associated with CS etiology. We review the genetic approaches used to understand molecular etiologies and pathogenic mechanisms for CS. Genes contributing to CS and associated vertebral malformation syndromes are also summarized.

Metrics

10 Record Views
1 citations in Scopus

Details

Logo image