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Journal article
A Case of Desmoplastic Small Round Cell Tumor
Journal of radiology case reports, v 9(8), pp 1-7
01 Aug 2015
PMID: 26629298
Featured in Collection : UN Sustainable Development Goals @ Drexel
Abstract
Desmoplastic small round cell tumor is a rare, aggressive tumor primarily affecting young males. It is considered a childhood cancer, and is characterized by a unique chromosomal translocation which leads to failure to suppress tumor growth. It is classified as a soft tissue sarcoma, sharing some features with other small round cell tumors such as Ewing's Sarcoma and primitive neuroectodermal tumor. Typical imaging findings include multiple heterogeneous, lobular abdominal masses, which can grow very large. Often there is a dominant mass with additional peritoneal, omental, retroperitoneal and retrovesical masses. Prognosis is relatively poor with a 3 year survival rate of 50% in those treated aggressively with surgical resection, chemotherapy, and radiation therapy. The clinical presentation, imaging characteristics and pathology are discussed in regards to a recent case.
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Details
- Title
- A Case of Desmoplastic Small Round Cell Tumor
- Creators
- David Reisner - Allegheny General HospitalDeborah Brahee - Allegheny General HospitalShweta Patel - Allegheny Gen Hosp, Dept ofPathol, Pittsburgh, PA 15212 USAMatthew Hartman - Allegheny General Hospital
- Publication Details
- Journal of radiology case reports, v 9(8), pp 1-7
- Publisher
- Edurad
- Number of pages
- 7
- Resource Type
- Journal article
- Language
- English
- Web of Science ID
- WOS:000443054300001
- Scopus ID
- 2-s2.0-84940660409
- Other Identifier
- 991021897487404721
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Data related to this publication, from InCites Benchmarking & Analytics tool:
- Web of Science research areas
- Radiology, Nuclear Medicine & Medical Imaging