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A functional ATG16L1 (T300A) variant is associated with necrotizing enterocolitis in premature infants
Journal article   Open access   Peer reviewed

A functional ATG16L1 (T300A) variant is associated with necrotizing enterocolitis in premature infants

Venkatesh Sampath, Vineet Bhandari, Jessica Berger, Daniel Merchant, Liyun Zhang, Mihoko Ladd, Heather Menden, Jeffery Garland, Namasivayam Ambalavanan, Neil Mulrooney, …
Pediatric research, v 81(4), pp 582-588
Apr 2017
PMID: 27893720
url
https://doi.org/10.1038/pr.2016.260View
Published, Version of Record (VoR)Maybe Open Access (Publisher Bronze) Open

Abstract

Alleles Autophagy Autophagy-Related Proteins - genetics Carrier Proteins - genetics Cohort Studies Enterocolitis, Necrotizing - genetics European Continental Ancestry Group Female Genetic Predisposition to Disease Genetic Variation Genotype Humans Infant, Newborn Infant, Premature Polymorphism, Single Nucleotide
The genetic basis of dysfunctional immune responses in necrotizing enterocolitis (NEC) remains unknown. We hypothesized that variants in nucleotide binding and oligomerization domain (NOD)-like receptors (NLRs) and autophagy (ATG) genes modulate vulnerability to NEC. We genotyped a multi-center cohort of premature infants with and without NEC for NOD1, NOD2, ATG16L1, CARD8, and NLRP3 variants. Chi-square tests and logistic regression were used for statistical analysis. In our primary cohort (n = 1,015), 86 (8.5%) infants developed NEC. The A allele of the ATG16L1 (Thr300Ala) variant was associated with increased NEC (AA vs. AG vs. GG; 11.3 vs. 8.4 vs. 4.8%, P = 0.009). In regression models for NEC that adjusted for epidemiological confounders, GA (P = 0.033) and the AA genotype (P = 0.038) of ATG16L1 variant were associated with NEC. The association between the A allele of the ATG16L1 variant and NEC remained significant among Caucasian infants (P = 0.02). In a replication cohort (n = 259), NEC rates were highest among infants with the AA genotype but did not reach statistical significance. We report a novel association between a hypomorphic variant in an autophagy gene (ATG16L1) and NEC in premature infants. Our data suggest that decreased autophagy arising from genetic variants may confer protection against NEC.

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Web of Science research areas
Pediatrics
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