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Journal article
Anesthetic Considerations for Patients with Hereditary Neuropathy with Liability to Pressure Palsies: A Narrative Review
Healthcare (Basel), v 12(8), 858
01 Apr 2024
PMID: 38667620
Featured in Collection : UN Sustainable Development Goals @ Drexel
Abstract
Hereditary neuropathy with liability to pressure palsies (HNPP) is an autosomal dominant demyelinating neuropathy characterized by an increased susceptibility to peripheral nerve injury from trauma, compression, or shear forces. Patients with this condition are unique, necessitating distinct considerations for anesthesia and surgical teams. This review describes the etiology, prevalence, clinical presentation, and management of HNPP and presents contemporary evidence and recommendations for optimal care for HNPP patients in the perioperative period. While the incidence of HNPP is reported at 7-16:100,000, this figure may be an underestimation due to underdiagnosis, further complicating medicolegal issues. With the subtle nature of symptoms associated with HNPP, patients with this condition may remain unrecognized during the perioperative period, posing significant risks. Several aspects of caring for this population, including anesthetic choices, intraoperative positioning, and monitoring strategy, may deviate from standard practices. As such, a tailored approach to caring for this unique population, coupled with meticulous preoperative planning, is crucial and requires a multidisciplinary approach.
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Details
- Title
- Anesthetic Considerations for Patients with Hereditary Neuropathy with Liability to Pressure Palsies: A Narrative Review
- Creators
- Krzysztof Laudanski - WinnMedOmar Elmadhoun - Mayo ClinicAmal Mathew - Drexel University, School of Biomedical Engineering, Science, and Health SystemsYul Kahn-Pascual - St George’s University Hospitals NHS Foundation TrustMitchell J. Kerfeld - Mayo ClinicJames Chen - Mayo ClinicDaniella C. Sisniega - University of PennsylvaniaFrancisco Gomez - University of Missouri
- Publication Details
- Healthcare (Basel), v 12(8), 858
- Publisher
- Mdpi
- Number of pages
- 14
- Resource Type
- Journal article
- Language
- English
- Academic Unit
- School of Biomedical Engineering, Science, and Health Systems
- Web of Science ID
- WOS:001210442900001
- Scopus ID
- 2-s2.0-85191464113
- Other Identifier
- 991022005884804721
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- Collaboration types
- Domestic collaboration
- International collaboration
- Web of Science research areas
- Health Care Sciences & Services
- Health Policy & Services