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Clinical manifestations and treatment of antisynthetase syndrome
Journal article   Peer reviewed

Clinical manifestations and treatment of antisynthetase syndrome

Joanna L. Marco and Bridget F. Collins
Best practice & research. Clinical rheumatology, v 34(4), 101503
Aug 2020
PMID: 32284267

Abstract

Anti-Jo-1 Antisynthetase antibody Antisynthetase syndrome Arthritis Idiopathic inflammatory myopathy Interstitial lung disease Mechanic's hands
Antisynthetase syndrome (ASyS) is an autoimmune disease clinically manifested most often by interstitial lung disease, myositis, and arthritis. Raynaud's syndrome, fever, and rashes are also commonly seen. This syndrome is characterized by the highly specific presence of antibodies against various aminoacyl transfer RNA synthetases, including Jo-1 and others. In this chapter, we provide an overview of ASyS, including pathogenesis, common clinical manifestations, and treatment strategies. We discuss the spectrum of disease seen with specific antisynthetase antibodies and examine the differences in phenotype between patients with different antisynthetase antibodies. We outline common treatment strategies, which should generally target the most severe and life- or organ-threatening disease manifestations. Finally, we discuss short- and long-term prognosis in ASyS.

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Web of Science research areas
Rheumatology
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