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Congenital Macroglossal Angiodysplasia (“Lymphangioendotheliomatosis”)
Journal article   Peer reviewed

Congenital Macroglossal Angiodysplasia (“Lymphangioendotheliomatosis”)

Ghazi Bakaeen, Sheldon Winkler, Lara Bakaeen, Lina A. Rehani and Christos D. Katsetos
Archives of pathology & laboratory medicine (1976), v 124(9), pp 1349-1351
01 Sep 2000
DOI: https://doi.org/10.5858/2000-124-1349-CMAL
PMID: 10975936
Featured in Collection :   UN Sustainable Development Goals @ Drexel

Abstract

Abstract A case of congenital lingual angiodysplasia with macroglossia in a 5-year-old girl is presented. A diffusely enlarged tongue was present at birth and continued to grow as the child aged. It was accompanied by impaired speech, difficulty in eating and breathing, and sleep apnea, necessitating surgical intervention. The fundamental lesion represents a complex vascular malformation of the lymphangioma-hemangioma type, involving extensively the deep musculature of the tongue. Multifocal and multicentric cavernous lymphangioma-like and hemangioma-like areas merge with benign angioendotheliomatous-like foci in a background of variable muscle degeneration and marked fibrosis. Neither a borderline nor an overtly malignant vasoformative neoplasm was present. Because of its distinctively widespread, multicentric intramuscular distribution, this lesion may be construed as a diffuse variant of lingual lymphangioma-hemangioma malformation, closely resembling a previously described case of macroglossal lymphangioendotheliomatosis.

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Collaboration types
Domestic collaboration
International collaboration
Web of Science research areas
Medical Laboratory Technology
Medicine, Research & Experimental
Pathology
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