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HLA-DQB1 Associations with Anti-topoisomerase-1 Antibodies in Patients with Systemic Sclerosis and their First Degree Relatives
Journal article   Peer reviewed

HLA-DQB1 Associations with Anti-topoisomerase-1 Antibodies in Patients with Systemic Sclerosis and their First Degree Relatives

Jean Whyte, Carol Artlett, Georgina Harvey, Clare O. Stephens, Ken Welsh, Carol Black, Peter J. Maddison and Neil J. McHugh
Journal of autoimmunity, v 7(4), pp 509-520
01 Aug 1994
PMID: 7980852

Abstract

The frequency and functional properties of anti-topoisomerase-1 antibodies (ATA) have been studied in 58 systemic sclerosis (SSc) probands, 218 first degree relatives and 22 spouses. The dependence of ATA on the presence of certain HLA-DRB1 and HLA-DQB1 alleles was examined. ATA were detected by immunodiffusion, by absorption or inhibition of topoisomerase-1 enzymic activity, by immunoblotting of a K562 cell extract and by immunoprecipitation of 35S radiolabelled cell lines. HLA class II typing for HLA-DRB1 and HLA-DQB1 was performed by oligonucleotide typing in 49 families. Six probands and two relatives and ATA. The relatives with ATA had SSc. All eight individuals with ATA directly inhibited topoisomerase-1 function. Four of the eight had limited skin disease and four had diffuse skin involvement. The seven who were genotyped had at least one HLA-DQB1 allele encoding for tyrosine at position 30 of the first domain. Therefore, ATA are not widely dispersed within families, but rather are only present in those with SSc, and certain genetic requirements appear necessary for their generation.

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Collaboration types
Domestic collaboration
Web of Science research areas
Immunology
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