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Inherited Interleukin 2-Inducible T-Cell (ITK) Kinase Deficiency in Siblings With Epidermodysplasia Verruciformis and Hodgkin Lymphoma
Journal article   Open access   Peer reviewed

Inherited Interleukin 2-Inducible T-Cell (ITK) Kinase Deficiency in Siblings With Epidermodysplasia Verruciformis and Hodgkin Lymphoma

Leila Youssefian, Hassan Vahidnezhad, Mehdi Yousefi, Amir Hossein Saeidian, Arghavan Azizpour, Andrew Touati, Neda Nikbakht, Kambiz Kamyab-Hesari, Mohammad Mahdi Adib-Sereshki, Sirous Zeinali, …
Clinical infectious diseases, v 68(11), pp 1938-1941
17 May 2019
PMID: 30778533
url
https://doi.org/10.1093/cid/ciy942View
Published, Version of Record (VoR) Open Open Access (License Unspecified)

Abstract

Life Sciences & Biomedicine Science & Technology Immunology Infectious Diseases Microbiology
Biallelic mutations in the ITK gene cause a T-cell primary immunodeficiency with Epstein-Barr virus (EBV)-lymphoproliferative disorders. We describe a novel association of a homozygous ITK mutation with -human papillomavirus (HPV)-positive epidermodysplasia verruciformis. Thus, loss of function in ITK can result in broad dysregulation of T-cell responses to oncogenic viruses, including -HPV and EBV.

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Collaboration types
Domestic collaboration
International collaboration
Web of Science research areas
Immunology
Infectious Diseases
Microbiology
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