Journal article
Neurofibromas of the Phrenic Nerve: A Case Report and Review of the Literature
World neurosurgery, v 88, pp 237-242
01 Apr 2016
PMID: 26746336
Featured in Collection : UN Sustainable Development Goals @ Drexel
Abstract
BACKGROUND: Phrenic neurofibromas are a rare pathologic entity, with 9 cases described in the English literature. They may occur in conjunction with or independently of neurofibromatosis type 1. Phrenic neurofibromas pose distinct therapeutic challenges compared with the more common phrenic schwannoma. We describe here a 12-year-old boy with neurofibroma of the left phrenic nerve presenting as dextroposition of the heart after paralysis of the left hemidiaphragm allowed herniation of abdominal contents into the left hemithorax and displaced the heart.
METHOD: Surgical resection of the tumor followed by diaphragmatic plication was performed to assess its degree of malignancy, reduce abdominal herniation, and improve lung capacity.
RESULTS: The operation markedly improved his hemidiaphragmatic elevation.
CONCLUSIONS: The spectrum of management options ranges from conservative surveillance to open thoracic surgery. Functional preservation of the phrenic nerve is technically challenging, and although phrenic neurofibromas often present with absent function that cannot be recovered, surgical intervention can be fruitful in restoring lung capacity through diaphragmatic reconstruction.
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Details
- Title
- Neurofibromas of the Phrenic Nerve: A Case Report and Review of the Literature
- Creators
- Michael G. Z. Ghali - Drexel UniversityVisish M. Srinivasan - Baylor Coll Med, Dept Neurosurg, Houston, TX 77030 USAAndrew Jea - Baylor College of MedicineJohn M. Slopis - The University of Texas MD Anderson Cancer CenterIan E. McCutcheon - The University of Texas MD Anderson Cancer Center
- Publication Details
- World neurosurgery, v 88, pp 237-242
- Publisher
- Elsevier
- Number of pages
- 6
- Resource Type
- Journal article
- Language
- English
- Web of Science ID
- WOS:000374649700035
- Scopus ID
- 2-s2.0-84959106507
- Other Identifier
- 991019312348404721
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- Collaboration types
- Domestic collaboration
- Web of Science research areas
- Clinical Neurology
- Surgery